Otology & Neurotology 39:e214–e215 2018, Otology & Neurotology, Inc. Imaging Case of the Month Unilateral Sensorineural Hearing Loss Presenting With Bilateral Temporal Bone Lesions Mark Sakai, Cameron C. Wick, and Joe Walter Kutz, Jr. Department of Otolaryngology—Head and Neck Surgery, University of Texas Southwestern Medical Center, Dallas, Texas A 15 year-old male presented with several months of Sporadic tumors have no sex predilection, while VHL- left-sided hearing loss and tinnitus. He reported no loss of related tumors have a 2:1 female predominance. The balance, vertigo, headaches, otalgia, or neurological most common VHL-related tumors are craniospinal impairment. Physical examination was unremarkable. hemangioblastomas occurring in 60 to 90% of patients Audiometry revealed left-sided profound sensorineural with VHL disease. ELST on the other hand have a less hearing loss and normal hearing on the right. predictable prevalence. The original incidence of ELST Computed tomography (CT) of the temporal bones in VHL disease was reported at 16% (2). A recent without contrast demonstrated expansion of the vestib- population-based study through the International Endo- ular aqueduct without erosion on the right (Fig. 1A). On lymphatic Sac Tumor Registry identified only 93 ELST the left there was an 11 14 19 mm
Otology & Neurotology – Wolters Kluwer Health
Published: Mar 1, 2018
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