Acta Neurol Belg (2017) 117:795–797 DOI 10.1007/s13760-017-0782-y LETTER TO THE EDITOR Subacute onset Hirayama disease with extensive myelopathy on MRI in ﬂexed posture 1 1 1 1,2 • • • Merel Brems Johan Van Goethem Mania De Praeter Barbara Willekens Received: 13 March 2017 / Accepted: 12 April 2017 / Published online: 25 April 2017 Belgian Neurological Society 2017 Introduction basketball at high level. The initial examination showed atrophy and decreased force on ﬁnger extension and Our case is an exceptional illustration of the proposed ﬂexion- abduction (MRC 4/5), more pronounced at the ulnar side. induced pathophysiology of Hirayama disease. Evidence, Pain nor sensory disturbances were present. Initial MRI privileging a mechanical pathophysiology, is growing and revealed a T2-hyperintense and atrophic cervical cord diagnostic inclusion criteria are involving MRI-conﬁrmed reaching from C4 to C7, initially suggesting a neuro-in- evidence of the mechanical pathophysiology. The forward ﬂammatory medullopathy (Fig. 1). However, extensive displacement of the posterior wall during neck ﬂexion is workup was negative in that aspect. Motor nerve conduc- considered to be the hallmark and primary pathophysiologic tion studies were normal with needle EMG showing evi- mechanism of this disease . In our case, the subacute onset dence of
Acta Neurologica Belgica – Springer Journals
Published: Apr 25, 2017
It’s your single place to instantly
discover and read the research
that matters to you.
Enjoy affordable access to
over 18 million articles from more than
15,000 peer-reviewed journals.
All for just $49/month
Query the DeepDyve database, plus search all of PubMed and Google Scholar seamlessly
Save any article or search result from DeepDyve, PubMed, and Google Scholar... all in one place.
Get unlimited, online access to over 18 million full-text articles from more than 15,000 scientific journals.
Read from thousands of the leading scholarly journals from SpringerNature, Elsevier, Wiley-Blackwell, Oxford University Press and more.
All the latest content is available, no embargo periods.
“Hi guys, I cannot tell you how much I love this resource. Incredible. I really believe you've hit the nail on the head with this site in regards to solving the research-purchase issue.”Daniel C.
“Whoa! It’s like Spotify but for academic articles.”@Phil_Robichaud
“I must say, @deepdyve is a fabulous solution to the independent researcher's problem of #access to #information.”@deepthiw
“My last article couldn't be possible without the platform @deepdyve that makes journal papers cheaper.”@JoseServera