Get 20M+ Full-Text Papers For Less Than $1.50/day. Start a 14-Day Trial for You or Your Team.

Learn More →

The Austrian Competence Network on Mastocytosis (AUCNM): a partner and part of the European ECNM network


The Austrian Competence Network on Mastocytosis (AUCNM): a partner and part of the European ECNM... Mastocytosis is a group of rare diseases characterized by abnormal expansion and accumulation of tissue mast cells in various organ systems. The disease can be divided into cutaneous and systemic variants. Although considered a rare pathologic condition, more and more patients are currently diagnosed as suffering from mastocytosis. The increasing incidence is best explained by enhanced awareness and improved diagnostics in the Western world. This has in turn created a need to establish optimal facilities for the diagnosis, management, and therapy of patients with mastocytosis. In 2002, the European Competence Network on Mastocytosis (ECNM) was established, with the aim to provide all available information to doctors and patients, and to improve management and therapy of mastocytosis in Europe. Within the ECNM, Centers of Excellence and Reference Centers have been defined and inaugurated. In addition, several countries established a local network of competence within the ECNM. In 2011, the Austrian Competence Network on Mastocytosis (AUCNM) was inaugurated. The AUCNM serves as an integral part and essential partner of the ECNM. In the current article, the structure, aims, achievements, and ongoing projects of the AUCNM are presented. http://www.deepdyve.com/assets/images/DeepDyve-Logo-lg.png memo - Magazine of European Medical Oncology Springer Journals

The Austrian Competence Network on Mastocytosis (AUCNM): a partner and part of the European ECNM network


Download PDF
5 pages

Loading next page...
 
/lp/springer-journals/the-austrian-competence-network-on-mastocytosis-aucnm-a-partner-and-UdW0miAiA5
Publisher
Springer Journals
Copyright
Copyright © 2013 by Springer-Verlag Wien
Subject
Medicine & Public Health; Oncology; Medicine/Public Health, general
ISSN
1865-5041
eISSN
1865-5076
DOI
10.1007/s12254-013-0083-y
Publisher site
See Article on Publisher Site

Abstract

Mastocytosis is a group of rare diseases characterized by abnormal expansion and accumulation of tissue mast cells in various organ systems. The disease can be divided into cutaneous and systemic variants. Although considered a rare pathologic condition, more and more patients are currently diagnosed as suffering from mastocytosis. The increasing incidence is best explained by enhanced awareness and improved diagnostics in the Western world. This has in turn created a need to establish optimal facilities for the diagnosis, management, and therapy of patients with mastocytosis. In 2002, the European Competence Network on Mastocytosis (ECNM) was established, with the aim to provide all available information to doctors and patients, and to improve management and therapy of mastocytosis in Europe. Within the ECNM, Centers of Excellence and Reference Centers have been defined and inaugurated. In addition, several countries established a local network of competence within the ECNM. In 2011, the Austrian Competence Network on Mastocytosis (AUCNM) was inaugurated. The AUCNM serves as an integral part and essential partner of the ECNM. In the current article, the structure, aims, achievements, and ongoing projects of the AUCNM are presented.

Journal

memo - Magazine of European Medical Oncology – Springer Journals

Published: May 1, 2013

References

  • Tissue mast cells in health and disease
    Parwaresch, MR; Horny, HP; Lennert, K.
  • Biology, classification and treatment of human mastocytosis
    Valent, P
  • Diagnosis and treatment of systemic mastocytosis: state of the art
    Valent, P; Akin, C; Sperr, WR
  • Systemic mastocytosis
    Akin, C; Metcalfe, DD
  • Diagnosis and classification of mast cell proliferative disorders: delineation from immunologic diseases and non-mast cell hematopoietic neoplasms
    Valent, P; Sperr, WR; Schwartz, LB; Horny, HP
  • Systemic mastocytosis: current concepts and treatment advances
    Tefferi, A; Pardanani, A
  • Mastocytosis: state of the art
    Horny, HP; Sotlar, K; Valent, P.
  • Mast cells and mastocytosis
    Metcalfe, DD
  • Pathogenesis, classification and treatment of mastocytosis: state of the art in 2010 and future perspectives
    Arock, M; Valent, P.
  • Rare forms of urticaria
    Nettleship, E; Tay, W.
  • Urticaria pigmentosa. A report of a case with autopsy
    Ellis, JM.
  • Mast cell leukemia? Malignant mastocytosis with leukemia-like manifestations
    Efrati, P; Klajman, A; Spitz, H.
  • Tissue mast cell leukemia
    Friedman, BI; Will, JJ; Freiman, DG; Braunstein, H
  • Mast cells and mast cell neoplasia: a review
    Lennert, K; Parwaresch, MR
  • Classification and diagnosis of mastocytosis: current status
    Metcalfe, DD
  • Identification of a point mutation in the catalytic domain of the protooncogene c-kit in peripheral blood mononuclear cells of patients who have mastocytosis with an associated hematologic disorder
    Nagata, H; Worobec, AS; Oh, CK
  • Somatic c-KIT activating mutation in urticaria pigmentosa and aggressive mastocytosis: establishment of clonality in a human mast cell neoplasm
    Longley, BJ; Tyrrell, L; Lu, SZ
  • Mutation analysis of C-KIT in patients with myelodysplastic syndromes without mastocytosis and cases of systemic mastocytosis
    Fritsche-Polanz, R; Jordan, JH; Feix, A
  • Indolent systemic mast cell disease in adults: immunophenotypic characterization of bone marrow mast cells and its diagnostic implications
    Escribano, L; Orfao, A; Díaz-Agustin, B
  • Diagnostic value of immunostaining for tryptase in patients with mastocytosis
    Horny, HP; Sillaber, C; Menke, D
  • Serum tryptase and the laboratory diagnosis of systemic mastocytosis
    Schwartz, LB; Irani, AM
  • Morphologic properties of neoplastic mast cells: delineation of stages of maturation and implication for cytological grading of mastocytosis
    Sperr, WR; Escribano, L; Jordan, JH
  • Diagnostic criteria and classification of mastocytosis: a consensus proposal
    Valent, P; Horny, HP; Escribano, L
  • Mast cell proliferative disorders: current view on variants recognized by the World Health Organization
    Valent, P; Akin, C; Sperr, WR; Horny, HP; Metcalfe, DD
  • Aggressive systemic mastocytosis and related mast cell disorders: current treatment options and proposed response criteria
    Valent, P; Akin, C; Sperr, WR
  • Systemic mastocytosis in 342 consecutive adults: survival studies and prognostic factors
    Lim, KH; Tefferi, A; Lasho, TL
  • WHO subvariants of indolent mastocytosis: clinical details and prognostic evaluation in 159 consecutive adults
    Pardanani, A; Lim, KH; Lasho, TL
  • Diagnosis, progression patterns and prognostication in mastocytosis
    Sperr, WR; Valent, P
  • Mastocytosis: current concepts in diagnosis and treatment
    Escribano, L; Akin, C; Castells, M; Orfao, A; Metcalfe, DD
  • Standards and standardization in mastocytosis: consensus statements on diagnostics, treatment recommendations and response criteria
    Valent, P; Akin, C; Escribano, L
  • Clonal mast cell disorders in patients with systemic reactions to Hymenoptera stings and increased serum tryptase levels
    Bonadonna, P; Perbellini, O; Passalacqua, G
  • Clinical, biological, and molecular characteristics of clonal mast cell disorders presenting with systemic mast cell activation symptoms
    Alvarez-Twose, I; González de Olano, D; Sánchez-Muñoz, L
  • Mastocytosis
    Brockow, K; Metcalfe, DD
  • Mast cell activation syndrome: Proposed diagnostic criteria
    Akin, C; Valent, P; Metcalfe, DD
  • Definitions, criteria and global classification of mast cell disorders with special reference to mast cell activation syndromes: a consensus proposal
    Valent, P; Akin, C; Arock, M
  • The European Competence Network on Mastocytosis (ECNM)
    Valent, P; Arock, M; Bischoff, SC
  • European Competence Network on Mastocytosis (ECNM): 10-year jubilee, update, and future perspectives
    Valent, P; Arock, M; Bonadonna, P