Abstract • Takayasu's arteritis (pulseless disease) is a vasculitis that affects the large arteries, including the aorta, its branches, and the pulmonary arteries. A 15-year-old girl with Takayasu's arteritis was referred to our institution for marked pulmonary hypertension in the absence of symptoms referable to systemic vasculitis. She was shown to have a thickened, narrowed thoracic aorta, a stenosed right axillary artery, and severely affected pulmonary arteries. Despite corticosteroid therapy she died one month after diagnosis. This patient's illness indicates that pulmonary vessels might be the principal vessels involved in Takayasu's arteritis. (AJDC 1986;140:372-374) References 1. Lupi HE, Sánchez TG, Horwitz S, et al: Pulmonary artery involvement in Takayasu's arteritis . Chest 1975;66:69-74.Crossref 2. Kawai C, Ishikawa K, Karo M, et al: 'Pulmonary pulseless disease': Pulmonary involvement in so-called Takayasu's disease . Chest 1978;73: 651-657.Crossref 3. Lupi HE, Sánchez TG, Marcushamer J, et al: Takayasu's arteritis: Clinical study of 107 cases . Am Heart J 1977;93:94-103.Crossref 4. Ueno A, Awane Y, Wakabayashi A, et al: Successfully operated obliterative brachiocephalic arteritis (Takayasu) associated with the elongated coarctation . Jpn Heart J 1967;8:538-544.Crossref 5. Numano F, Isohisa I, Kishi U, et al: Takayasu's disease in twin sisters . Circulation 1978;58:173-177.Crossref 6. Kaplinski C, Frand M, Rubinstein Z: Fever of unknown origin as a manifestation of Takayasu disease . Harefuah 1979;96:659-664. 7. Nakao K, Ikeda M, Kimota S, et al: Takayasu's arteritis: Clinical report of 84 cases and immunologic studies of seven cases . Circulation 1967;35:1141-1155.Crossref 8. Ueda H, Morooka S, Ito I, et al: Clinical observation of 107 cases . Jpn Heart J 1969;10: 277-288.Crossref 9. Ikeda M: Immunologic studies on Takayasu's arteritis . Jpn Circ J 1966;30:87-89.Crossref 10. Ask-Upmark E: On the 'pulseless disease' outside of Japan . Acta Med Scand 1954;149: 161-178.Crossref 11. Plachecka M, Kopec M, Kowalska M: Rheumatoid factor in Takayasu syndrome . Scand J Rheumatol 1966;12:29-34.
American Journal of Diseases of Children – American Medical Association
Published: Apr 1, 1986