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Successful Treatment of Keratoderma Hereditaria Mutilans With an Aromatic Retinoid

Successful Treatment of Keratoderma Hereditaria Mutilans With an Aromatic Retinoid Abstract † Clinical features and treatment of keratoderma hereditaria mutilans (Vohwinkel's syndrome) are described in an 11-year-boy. The disease, in particular the mutilating complications (pseudo-ainhum), responded satisfactorily to the oral administration of etretinate, an aromatic retinoid. (Arch Dermatol 1981;117:225-228) References 1. Vohwinkel KH: Keratoderma hereditarium mutilans . Arch Dermatol Syphil 1929;158:354-364.Crossref 2. Gibbs RC, Frank SB: Keratoderma hereditaria mutilans (Vohwinkel): Differentiating features of conditions with constriction of digits . Arch Dermatol 1966;94:619-625.Crossref 3. Piers F: Hereditary keratodermia and ainhum . Br J Dermatol 1967;79:693-698.Crossref 4. Greschebin S: Observations on ainhum: Does it exist as an entity . Urol Cut Rev 1936;40:98-102. 5. Wirz F: Keratoma hereditarium mutilans: Zu dem Aufsatz von K. H. Vohwinkel . Arch Dermatol Syphil 1930;159:311-312.Crossref 6. Drummond A: A case of unusual skin lesions . Ir J Med Sci 1938;85:85-89. 7. Schimpf A: Zur systematischen Anwendung eines aromatischen Vitamin-A-Saure-Derivate (Ro 10-9359) bei psoriasis und Keratosen . Z Haut Geschlkrankh 1976;51:265-274. 8. Ebling FJ, Rook A: Diffuse palmoplantar keratoderma , in Rook A (ed): Textbook of Dermatology . Oxford, England, Blackwell Scientific Publications, 1972, pp 1179-1181. 9. Greither A: Erbliche Palmoplantar Keratosen . Hautarzt 1977;28:395-403. 10. Greither A: Keratosis palmoplantaris mit peridontopathie (Papillon-Lefèvre) . Dermatologica 1959;119:248-263.Crossref 11. Sjögren T, Larsson T: Oligophrenia in combination with congenital ichthyosis and spastic disorders: A clinical and genetic study . Acta Psychiatr Scand 1957;32:113-123.Crossref 12. Reed ML, Stanley J, Stengel F, et al: Mal de Meleda treated with 13-cis retinoid acid . Arch Dermatol 1979;115:605-608.Crossref 13. Davies MC, Greaves MW, Marks R: Non-bullous ichthyosiform erythroderma with annular digital constrictions . Br J Dermatol 1979;101:38-40.Crossref 14. Matter A, Bollag W: A fine structural study on the therapeutic effect of aromatic retinoid on chemically induced skin papillomas of the mouse . Eur J Cancer 1977;13:831-838.Crossref 15. Wolff HH, Christophers E, Braun Falco O: Beeinflussung der epidermalen Ausdifferenzierung durch Vitamin-A-Säure: Eine Elektronenmikroskopische Untersuchung . Arch Klin Exp Derm 1970;237:774-795.Crossref 16. Prutkin L: The effect of vitamin A acid on hyperkeratinization and the kerato-acanthoma . J Invest Dermatol 1967;49:165-172.Crossref 17. Cole GJ: Ainhum: An account of 54 patients with special reference to etiology and treatment . J Bone Joint Surg Br 1965;47:43-51. http://www.deepdyve.com/assets/images/DeepDyve-Logo-lg.png Archives of Dermatology American Medical Association

Successful Treatment of Keratoderma Hereditaria Mutilans With an Aromatic Retinoid

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Publisher
American Medical Association
Copyright
Copyright © 1981 American Medical Association. All Rights Reserved.
ISSN
0003-987X
eISSN
1538-3652
DOI
10.1001/archderm.1981.01650040041018
Publisher site
See Article on Publisher Site

Abstract

Abstract † Clinical features and treatment of keratoderma hereditaria mutilans (Vohwinkel's syndrome) are described in an 11-year-boy. The disease, in particular the mutilating complications (pseudo-ainhum), responded satisfactorily to the oral administration of etretinate, an aromatic retinoid. (Arch Dermatol 1981;117:225-228) References 1. Vohwinkel KH: Keratoderma hereditarium mutilans . Arch Dermatol Syphil 1929;158:354-364.Crossref 2. Gibbs RC, Frank SB: Keratoderma hereditaria mutilans (Vohwinkel): Differentiating features of conditions with constriction of digits . Arch Dermatol 1966;94:619-625.Crossref 3. Piers F: Hereditary keratodermia and ainhum . Br J Dermatol 1967;79:693-698.Crossref 4. Greschebin S: Observations on ainhum: Does it exist as an entity . Urol Cut Rev 1936;40:98-102. 5. Wirz F: Keratoma hereditarium mutilans: Zu dem Aufsatz von K. H. Vohwinkel . Arch Dermatol Syphil 1930;159:311-312.Crossref 6. Drummond A: A case of unusual skin lesions . Ir J Med Sci 1938;85:85-89. 7. Schimpf A: Zur systematischen Anwendung eines aromatischen Vitamin-A-Saure-Derivate (Ro 10-9359) bei psoriasis und Keratosen . Z Haut Geschlkrankh 1976;51:265-274. 8. Ebling FJ, Rook A: Diffuse palmoplantar keratoderma , in Rook A (ed): Textbook of Dermatology . Oxford, England, Blackwell Scientific Publications, 1972, pp 1179-1181. 9. Greither A: Erbliche Palmoplantar Keratosen . Hautarzt 1977;28:395-403. 10. Greither A: Keratosis palmoplantaris mit peridontopathie (Papillon-Lefèvre) . Dermatologica 1959;119:248-263.Crossref 11. Sjögren T, Larsson T: Oligophrenia in combination with congenital ichthyosis and spastic disorders: A clinical and genetic study . Acta Psychiatr Scand 1957;32:113-123.Crossref 12. Reed ML, Stanley J, Stengel F, et al: Mal de Meleda treated with 13-cis retinoid acid . Arch Dermatol 1979;115:605-608.Crossref 13. Davies MC, Greaves MW, Marks R: Non-bullous ichthyosiform erythroderma with annular digital constrictions . Br J Dermatol 1979;101:38-40.Crossref 14. Matter A, Bollag W: A fine structural study on the therapeutic effect of aromatic retinoid on chemically induced skin papillomas of the mouse . Eur J Cancer 1977;13:831-838.Crossref 15. Wolff HH, Christophers E, Braun Falco O: Beeinflussung der epidermalen Ausdifferenzierung durch Vitamin-A-Säure: Eine Elektronenmikroskopische Untersuchung . Arch Klin Exp Derm 1970;237:774-795.Crossref 16. Prutkin L: The effect of vitamin A acid on hyperkeratinization and the kerato-acanthoma . J Invest Dermatol 1967;49:165-172.Crossref 17. Cole GJ: Ainhum: An account of 54 patients with special reference to etiology and treatment . J Bone Joint Surg Br 1965;47:43-51.

Journal

Archives of DermatologyAmerican Medical Association

Published: Apr 1, 1981

References