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LIPOID GRANULOMATOSIS (HAND-SCHÜLLER-CHRISTIAN DISEASE) INVOLVING THE MIDDLE EAR AND TEMPORAL BONE

LIPOID GRANULOMATOSIS (HAND-SCHÜLLER-CHRISTIAN DISEASE) INVOLVING THE MIDDLE EAR AND TEMPORAL BONE Abstract Lipoid granulomatosis (type Hand-Schüller-Christian disease) occurring in an adult and with diffuse involvement of the middle ear and temporal bone as the sole manifestation of the disease is uncommon. The relative rarity of the condition as evidenced by the paucity of reports in the literature, as well as the extreme difficulty of establishing the diagnosis in this case and the excellent therapeutic result after intensive roentgen therapy, warrant the present report as well as a brief discussion of lipoid granulomatosis. REPORT OF A CASE R. H., a woman aged 50, was first observed in the outpatient clinic of the Mount Sinai Hospital on Jan. 6, 1936, with the chief complaint of gradual onset of pain and deafness in the left ear of four years' duration. The pain, which had become continuous, was accompanied by buzzing. Four months prior to admission the patient suffered episodes of transitory facial paralysis and postauricular References 1. Panzer, T.: Doppeltbrechende Substanzen aus pathologischen Organen , Ztschr. f. physiol. Chem. 54:239-254, 1907.Crossref 2. Pinkus, F., and Pick, L.: Zur Struktur und Genese der symptomatische Xanthome , Deutsche med. Wchnschr. 34:1426-1431, 1908.Crossref 3. Chester, W.: Ueber Lipoidgranulomatose , Virchows Arch. f. path. Anat. 279:561-602, 1930.Crossref 4. Christian, H. A.: Defects in Membranous Bones, Exophthalmos and Diabetes Insipidus , in Contributions to Medical & Biologic Research Dedicated to Sir William Osler, in Honor of His Seventieth Birthday , July 12, 1919, by His Pupils and Coworkers, New York, Paul B. Hoeber, 1919, vol. 1, p. 390. 5. Chiari, H.: Die generalisierte Xanthomatose von Typus Schüller-Christian , Ergebn. d. allg. Path. u. path. Anat. 24:396-450, 1931. 6. Ighenti, W. K.: Zur Frage der allgemeinen granulomatösen Xanthomatose , Virchows Arch. f. path. Anat. 282:585-612, 1931.Crossref 7. Rowland, R. S.: Xanthomatosis and the Reticulo-Endothelial System , Arch. Int. Med. 42:611-674 ( (Nov.) ) 1928.Crossref 8. Chester, W., and Kugel, V. H.: Lipoid Granulomatosis (Type Hand-Schüller-Christian) , Arch. Path. 14:595-612 ( (Nov.) ) 1932. 9. Berman, W.: Xanthomatosis (Lipoid Histiocytosis) of the Spine , J. Mt. Sinai Hosp. 5:419-425 ( (Nov.) -Dec.) 1938. 10. Lederer, F. L.; Poncher, H. G., and Fabricant, N. D.: Aural Manifestations of Lipoid Granulomatosis of the Skull , Arch. Otolaryng. 21:27-40 ( (Jan.) ) 1935.Crossref 11. Schüller, A.: Ueber eigenartige Schädeldefekte in Jugendalter , Fortschr. a. d. Geb. d. Röntgenstrahlen 23:12-18, 1915. 12. Höfer, K.: Beitrag zur Xanthomatose der Dura mater und der Schädelknochen, Schädeldefekte, Exophthalmos Diabetes insipidus, Zwergwuchs) , Klin. Wchnschr. 9:1302-1305 ( (July 12) ) 1930.Crossref 13. Sosman, M. C.: Xanthomatosis, Schüller-Christian Disease, Lipoid Histiocytosis , J. A. M. A. 98:110-117 ( (Jan. 9) ) 1932.Crossref 14. Gilmore, M. E.: Multiple Myeloma Syndrome in a Child , Texas State J. Med. 21:358-362 ( (Oct.) ) 1925. 15. Cignolini, P.: Effetti locali e generali della radioterapia in un caso di diabete insipido associato ad osteopatia , Radiol. med. 16:16-21 ( (Jan.) ) 1929. 16. Vampré, E.: Syndrome de Christian , Rev. sud.-am. de méd. et de chir. 1:459-464 ( (May) ) 1930. 17. Shea, J. J.: Xanthomatosis (Schüller-Christian Disease): Report of a Case in Which There Was a Radiosensitive Pathologic Growth in the Mastoid , Arch. Otolaryng. 28:1035-1036 ( (Dec.) ) 1938. 18. Wood, V. V.: Bilateral Xanthomatosis (Lipoidosis) of the Mastoid: Case Report , Ann. Otol., Rhin. & Laryng. 46:991-1008 ( (Dec.) ) 1937. 19. Schall, L. A., in discussion on Shea.17 http://www.deepdyve.com/assets/images/DeepDyve-Logo-lg.png Archives of Otolaryngology American Medical Association

LIPOID GRANULOMATOSIS (HAND-SCHÜLLER-CHRISTIAN DISEASE) INVOLVING THE MIDDLE EAR AND TEMPORAL BONE

Archives of Otolaryngology , Volume 32 (6) – Dec 1, 1940

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Publisher
American Medical Association
Copyright
Copyright © 1940 American Medical Association. All Rights Reserved.
ISSN
0003-9977
DOI
10.1001/archotol.1940.00660021053005
Publisher site
See Article on Publisher Site

Abstract

Abstract Lipoid granulomatosis (type Hand-Schüller-Christian disease) occurring in an adult and with diffuse involvement of the middle ear and temporal bone as the sole manifestation of the disease is uncommon. The relative rarity of the condition as evidenced by the paucity of reports in the literature, as well as the extreme difficulty of establishing the diagnosis in this case and the excellent therapeutic result after intensive roentgen therapy, warrant the present report as well as a brief discussion of lipoid granulomatosis. REPORT OF A CASE R. H., a woman aged 50, was first observed in the outpatient clinic of the Mount Sinai Hospital on Jan. 6, 1936, with the chief complaint of gradual onset of pain and deafness in the left ear of four years' duration. The pain, which had become continuous, was accompanied by buzzing. Four months prior to admission the patient suffered episodes of transitory facial paralysis and postauricular References 1. Panzer, T.: Doppeltbrechende Substanzen aus pathologischen Organen , Ztschr. f. physiol. Chem. 54:239-254, 1907.Crossref 2. Pinkus, F., and Pick, L.: Zur Struktur und Genese der symptomatische Xanthome , Deutsche med. Wchnschr. 34:1426-1431, 1908.Crossref 3. Chester, W.: Ueber Lipoidgranulomatose , Virchows Arch. f. path. Anat. 279:561-602, 1930.Crossref 4. Christian, H. A.: Defects in Membranous Bones, Exophthalmos and Diabetes Insipidus , in Contributions to Medical & Biologic Research Dedicated to Sir William Osler, in Honor of His Seventieth Birthday , July 12, 1919, by His Pupils and Coworkers, New York, Paul B. Hoeber, 1919, vol. 1, p. 390. 5. Chiari, H.: Die generalisierte Xanthomatose von Typus Schüller-Christian , Ergebn. d. allg. Path. u. path. Anat. 24:396-450, 1931. 6. Ighenti, W. K.: Zur Frage der allgemeinen granulomatösen Xanthomatose , Virchows Arch. f. path. Anat. 282:585-612, 1931.Crossref 7. Rowland, R. S.: Xanthomatosis and the Reticulo-Endothelial System , Arch. Int. Med. 42:611-674 ( (Nov.) ) 1928.Crossref 8. Chester, W., and Kugel, V. H.: Lipoid Granulomatosis (Type Hand-Schüller-Christian) , Arch. Path. 14:595-612 ( (Nov.) ) 1932. 9. Berman, W.: Xanthomatosis (Lipoid Histiocytosis) of the Spine , J. Mt. Sinai Hosp. 5:419-425 ( (Nov.) -Dec.) 1938. 10. Lederer, F. L.; Poncher, H. G., and Fabricant, N. D.: Aural Manifestations of Lipoid Granulomatosis of the Skull , Arch. Otolaryng. 21:27-40 ( (Jan.) ) 1935.Crossref 11. Schüller, A.: Ueber eigenartige Schädeldefekte in Jugendalter , Fortschr. a. d. Geb. d. Röntgenstrahlen 23:12-18, 1915. 12. Höfer, K.: Beitrag zur Xanthomatose der Dura mater und der Schädelknochen, Schädeldefekte, Exophthalmos Diabetes insipidus, Zwergwuchs) , Klin. Wchnschr. 9:1302-1305 ( (July 12) ) 1930.Crossref 13. Sosman, M. C.: Xanthomatosis, Schüller-Christian Disease, Lipoid Histiocytosis , J. A. M. A. 98:110-117 ( (Jan. 9) ) 1932.Crossref 14. Gilmore, M. E.: Multiple Myeloma Syndrome in a Child , Texas State J. Med. 21:358-362 ( (Oct.) ) 1925. 15. Cignolini, P.: Effetti locali e generali della radioterapia in un caso di diabete insipido associato ad osteopatia , Radiol. med. 16:16-21 ( (Jan.) ) 1929. 16. Vampré, E.: Syndrome de Christian , Rev. sud.-am. de méd. et de chir. 1:459-464 ( (May) ) 1930. 17. Shea, J. J.: Xanthomatosis (Schüller-Christian Disease): Report of a Case in Which There Was a Radiosensitive Pathologic Growth in the Mastoid , Arch. Otolaryng. 28:1035-1036 ( (Dec.) ) 1938. 18. Wood, V. V.: Bilateral Xanthomatosis (Lipoidosis) of the Mastoid: Case Report , Ann. Otol., Rhin. & Laryng. 46:991-1008 ( (Dec.) ) 1937. 19. Schall, L. A., in discussion on Shea.17

Journal

Archives of OtolaryngologyAmerican Medical Association

Published: Dec 1, 1940

References