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Dietary Treatment of Maple Syrup Urine Disease

Dietary Treatment of Maple Syrup Urine Disease Abstract ABOUT three years ago, the dietary treatment of a newborn infant with maple syrup urine disease was reported (Westall, 19631). At that time, the child was 15 months old and the belief was expressed that the child's mental and neurological status was normal and that the controlled diet had prevented the serious cerebro-degenerative changes which occur when this disease is untreated. The purpose of this paper is to report on the further progress of this child, now nearly 5 years old. When 5½ months old, the patient was allowed to go home. Her mother was instructed in the preparation of the diet by a dietitian and she was provided with the necessary equipment. Apart from occasional short stays in hospital, not exceeding two weeks at any one time, the child has been cared for at home since that time. She now attends a nursery school for physically handicapped children References 1. Westall, R.G.: Dietary Treatment of a Child With Maple Syrup Urine Disease (Branched-Chain Ketoaciduria) , Arch Dis Child 38:485, 1963.Crossref http://www.deepdyve.com/assets/images/DeepDyve-Logo-lg.png American Journal of Diseases of Children American Medical Association

Dietary Treatment of Maple Syrup Urine Disease

American Journal of Diseases of Children , Volume 113 (1) – Jan 1, 1967

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Publisher
American Medical Association
Copyright
Copyright © 1967 American Medical Association. All Rights Reserved.
ISSN
0002-922X
DOI
10.1001/archpedi.1967.02090160108011
Publisher site
See Article on Publisher Site

Abstract

Abstract ABOUT three years ago, the dietary treatment of a newborn infant with maple syrup urine disease was reported (Westall, 19631). At that time, the child was 15 months old and the belief was expressed that the child's mental and neurological status was normal and that the controlled diet had prevented the serious cerebro-degenerative changes which occur when this disease is untreated. The purpose of this paper is to report on the further progress of this child, now nearly 5 years old. When 5½ months old, the patient was allowed to go home. Her mother was instructed in the preparation of the diet by a dietitian and she was provided with the necessary equipment. Apart from occasional short stays in hospital, not exceeding two weeks at any one time, the child has been cared for at home since that time. She now attends a nursery school for physically handicapped children References 1. Westall, R.G.: Dietary Treatment of a Child With Maple Syrup Urine Disease (Branched-Chain Ketoaciduria) , Arch Dis Child 38:485, 1963.Crossref

Journal

American Journal of Diseases of ChildrenAmerican Medical Association

Published: Jan 1, 1967

References