Abstract We report a case of cor triatriatum in a 4-year-old girl on whom precise anatomic diagnosis was made preoperatively by cardiac catheterization and angiocardiography. The anomalous septum was removed through successful surgery. The condition had been diagnosed two years earlier as pulmonary hypertension secondary to a ventricular septal defect, in spite of a high pulmonary artery wedge pressure (PAWP). We emphasize the importance of the PAWP in separating pulmonary venous hypertension from other forms of pulmonary hypertension since this subgroup is usually operable and even curable if surgery is performed before irreversible pulmonary vascular changes occur. In spite of the small risk, we feel that angiocardiographic studies are necessary to demonstrate the anomalous septum. References 1. Miller GAH, Ongley PA, Anderson MW, et al: Cor triatriatum, hemodynamic and angiocardiographic diagnosis . Amer Heart J 68:298-304, 1964.Crossref 2. Perry LW, Scott LP III, McClenathan JE: Cor triatriatum: Preoperative diagnosis and successful surgical repair in a small infant . J Pediat 71:840-847, 1967.Crossref 3. Niwayama G: Cor triatriatum . Amer Heart J 59:291-317, 1960.Crossref 4. Hamilton WF: Circulation , in Handbook of Physiology . Washington, DC, American Physiological Society, 1963, section 2, pp 1687-1688. 5. Harris P, Heath D: The Human Pulmonary Circulation . Baltimore, Williams & Wilkins, 1962, pp 52-55. 6. Blount SG Jr: Primary pulmonary hypertension . Mod Conc Cardiovasc Dis 36:67-72, 1967. 7. Schafer H, Blain JM, Ceballos R, et al: Essential pulmonary hypertension: Report of clinical-physiologic studies in three patients, with death following catheterization of the heart . Ann Intern Med 44:505-523, 1956.Crossref 8. Lam CR, Green E, Drake E: Diagnosis and treatment of two types of triatrial heart . Surgery 51:127-137, 1962. 9. LaSalle R, Ethier M, Stanley P, et al: Cor triatriatum: Report of a case with emphasis on cineangiocardiography . Canad Med Assoc J 89:616-620, 1963. 10. Ellis K, Griffiths SP, Jesse MJ: Cor triatriatum: Angiocardiographic demonstration of the obstructing left atrial membrane . Amer J Roentgen 92:669-675, 1964. 11. Neufeld HN, Pauzner Y, Gueron M, et al: Cor triatriatum: Report of case successfully operated with special reference to angiocardiographic diagnosis . Israel J Med Sci 1:71-78, 1965. 12. Girod DA, Kurlander GJ: Diagnosis of cor triatriatum by left ventricular angiography: Report of a case . Dis Chest 50: 535-538, 1966.Crossref 13. Soverville J: Masked cor triatriatum . Brit Heart J 28:55-61, 1966.Crossref 14. Wolfe RR, Ruttenberg HD, Desilets DT, et al: Cor triatriatum: Total correction in an infant . J Thorac Cardiovasc Surg 56:114-119, 1968.
American Journal of Diseases of Children – American Medical Association
Published: May 1, 1972