TY - JOUR
AU - Mueller, Rita J.
AB - Abstract • An audiologic study of a 54-year-old patient with Charcot-Marie-Tooth disease whose initial symptom was hearing difficulty is presented. While findings from basic audiologic tests were not consistent with the degree of auditory difficulty reported by the patient, special testing did indicate a notable deficit. Although the auditory periphery was probably mildly involved, it seemed that the major auditory deficit was central. (Arch Otolaryngol 1982;108:595-599) References 1. Cruse R, Conomy J, Wilbourne A, et al: Heredity hypertrophic neuropathy combining features of tic douloureux, Charcot-Marie-Tooth disease, and deafness . Cleve Clin Q 1977;44:107-111. 2. Hollinger PC, Hollinger LD, Vuckovich DM, et al: Bilateral abductor vocal cord paralysis in Charcot-Marie-Tooth disease . Ann Otol 1979; 88:205-209. 3. Harrison TR (ed): Principals of Internal Medicine , ed 4. New York, McGraw-Hill Book Co, 1962, pp 1870-1911. 4. Dyck PJ, Lambert EH: Lower motor and primary sensory neuron diseases with peroneal muscular atrophy: II. Neurologic, genetic, and electrophysiologic findings in various neuronal degenerations . Arch Neurol 1968;18:619-625.Crossref 5. Rosenberg RN, Chutorian A: Familial opticoacoustic nerve degeneration and polyneuropathy . Neurology 1967;17:827-832.Crossref 6. Dyck PJ, Thomas PK, Lambert EH: Peripheral Neuropathy . Philadelphia, WB Saunders Co, 1975, vol 2, pp 834-855. 7. Tackmann W, Rad E: Pattern shift visual evoked potentials in Charcot-Marie-Tooth disease . J Neurol 1980;224:71-74.Crossref 8. Tillman T, Carhart R: An Expanded Test for Speech Discrimination Utilizing CNC Monosyllabic Words, technical report 8AM-TR-66-55. Brooks AFB, Tex, USAF School of Aerospace Medicine, Aerospace Medical Division, 1966. 9. Bess F, Josey A, Humes L: Performance intensity functions in cochlear and eighth nerve disorders . Am J Otol 1979;1:27-31. 10. Carhart R: Clinical determination of abnormal auditory adaptation . Arch Otolaryngol 1957;65:32-39.Crossref 11. Noffsinger D, Olsen W, Carhart R, et al: Auditory and vestibular aberrations in multiple sclerosis . Acta Otolaryngol 1972;303( (suppl) ):1-58. 12. Willeford J, Billiger J: Auditory perception in children with learning disabilities , in Katz J (ed): Handbook of Clinical Audiology . Baltimore, Williams & Wilkins Co, 1978, pp 252-261. 13. Katz J: The use of staggered spondaic words for assessing integrity of the central auditory nervous system . J Aud Res 1962;1:327-337. 14. Brunt M: The staggered spondaic word test , in Katz J (ed): Handbook of Clinical Audiology . Baltimore, Williams & Wilkins Co, 1978, pp 262-274. 15. Katz J: The staggered spondaic word test , in Keith R (ed): Central Auditory Dysfunction . New York, Grune & Stratton Inc, 1977, pp 103-121. 16. Musiek F, Wilson D: SSW and dichotic digit results pre- and postcommissurotomy: A case report . J Speech Hear Dis 1979;44:528-533. 17. Pinheiro M, Ptacek R: Reversals in the perception of noise and tone patterns . J Acoust Soc Am 1971;49:1778-1782.Crossref 18. Carhart R: Special hearing tests for otoneurologic diagnosis . Arch Otolaryngol 1969; 89:64-67.Crossref 19. Dublin W: Fundamentals of Sensorineural Auditory Pathology . Springfield, Ill, Charles C Thomas Publishers, 1976. 20. Jerger J, Jerger S: Auditory findings in brain stem disorders . Arch Otolaryngol 1974; 99:342-350.Crossref 21. Jerger J, Jerger S: Diagnostic significance of PB word functions . Arch Otolaryngol 1971; 93:573-580.Crossref 22. Starr A, Achor L: Auditory brain stem responses in neurological disease . Arch Neurol 1975;32:761-768.Crossref 23. Selters W, Brackmann D: Brain stem electric response audiometry in acoustic tumor detection , in House W, Luetje C (eds): Acoustic Tumors . Baltimore, University Park Press, 1979, vol 1, pp 225-236. 24. Colleti V: Stapedius reflex abnormalities in multiple sclerosis . Audiology 1975;14:63-69.Crossref 25. Anderson H, Barr B, Wedenberg E: Early diagnosis of eighth nerve tumors by acoustic reflex tests . Acta Otolaryngol 1970;263 ( (suppl) ):232-238.Crossref 26. Olsen W, Noffsinger D: Comparison of one new and three old tests of auditory adaptation . Arch Otolaryngol 1974;99:94-99.Crossref 27. Tillman T: Special hearing tests in otoneurologic diagnosis . Arch Otolaryngol 1969;89:25-30.Crossref 28. Johnson E: Auditory findings in 200 cases of acoustic neuromas . Arch Otolaryngol 1968; 88:598-603.Crossref 29. Menzel O, Finney L, David N, et al: Atypical audiologic findings in a case of acoustic neuroma . Laryngoscope 1964;74:1391-1400.Crossref 30. Parker W, Decker R, Richards N: Auditory function and lesions of the pons . Arch Otolaryngol 1968;87:26-38.Crossref 31. Palva T, Kärjä J, Palva A: Forward vs reversed Bekesy tracings . Arch Otolaryngol 1970;91:449-452.Crossref 32. Jerger J, Jerger S, Mauldin L: The forward-backward discrepancy in Bekesy audiometry . Arch Otolaryngol 1972;96:400-411.Crossref 33. Wright H: Brief tone audiometry , in Katz J (ed): Handbook of Clinical Audiology. Baltimore, Williams & Wilkins Co, 1978, pp 218-230. 34. Feldman A: Acoustic impedance admittance battery , in Katz J (ed): Handbook of Clinical Audiology . Baltimore, Williams & Wilkins Co, 1978, pp 356-372. 35. Olsen W, Noffsinger D: Masking level differences for cochlear and brain stem lesions . Ann Otol Rhinol Laryngol 1976;85:820-825. 36. Lynn G, Gilroy J: Perception of rapidly alternating speech in patients with brain stem and cerebral hemisphere lesions. Read before the ninth Colorado Otology-Audiology Workshop, Vail, Colo, March 3, 1975. 37. Smith B, Resnick D: An auditory test for assessing brain stem integrity: Preliminary report . Laryngoscope 1972;82:414-424.Crossref 38. Durlach N, Thompson C, Colburn H: Binaural interaction in impaired listeners . Audiology 1981;20:181-211.Crossref 39. Olsen W, Noffsinger D, Carhart R: Masking level differences encountered in clinical populations . Audiology 1976;15:287-301.Crossref 40. Bocca E, Calearo C: Central hearing processes , in Jerger J (ed): Modern Developments in Audiology . New York, Academic Press Inc, 1963, pp 337-370. 41. Lynn G, Gilroy J: Effects of brain lesions on the perception of monotic and dichotic speech stimuli , in Sullivan M (ed): Central Auditory Processing Disorders . Omaha, University of Nebraska, 1975, pp 47-82. 42. Korsan-Bengsten M: Distorted speech audiometry . Acta Otolaryngol 1973;310( (suppl) ):10-56. 43. Kimura D: Some effects of temporal lobe damage on auditory perception . Can J Psychol 1961;15:156-165.Crossref 44. Pinheiro M: Auditory pattern perception in patients with right and left hemisphere lesions . Ohio J Speech Hear 1976;12:9-20. 45. Miltenberger G, Dawson G, Raica A: Central auditory testing with peripheral hearing loss . Arch Otolaryngol 1978;104:11-15.Crossref 46. Roeser R, Johns D, Price L: Dichotic listening in adults with sensorineural hearing loss . J Am Aud Soc 1976;2:19-25.
TI - Audiologic Findings in Charcot-Marie-Tooth Disease
JO - Archives of Otolaryngology
DO - 10.1001/archotol.1982.00790570061015
DA - 1982-09-01
UR - https://www.deepdyve.com/lp/american-medical-association/audiologic-findings-in-charcot-marie-tooth-disease-r4DEiHB00p
SP - 595
EP - 599
VL - 108
IS - 9
DP - DeepDyve
ER -