TY - JOUR AU - Frank, Marlies AB - Acta Diabetol (2017) 54:979–980 DOI 10.1007/s00592-017-1029-3 LETTER TO THE EDITOR Maternally inherited diabetes and deafness is a mitochondrial multiorgan disorder syndrome (MIMODS) 1 2 Josef Finsterer  · Marlies Frank   Received: 5 June 2017 / Accepted: 14 July 2017 / Published online: 29 July 2017 © Springer-Verlag Italia S.r.l. 2017 Keywords Mitochondrial · mtDNA · Phenotype · manifestations were clinically or subclinically present in Genotype · Myopathy · Muscle biopsy the presented patient? We should be informed about the detailed sequence of clinical manifestations arising during the disease course. Letter to the Editor Involvement of other organs often becomes clinically evident in the course of infectious disease or application of With interest, we read the article by Ko et al. about a 22yo new drugs [4]. Which was the trigger of ketoacidosis and female with maternally inherited diabetes and deafness hyperglycemia? (MIDD) due to the mutation m.3243A > G who manifested We do not agree with the statement that chorea-ballism initially with chorea-ballism [1]. We have the following was the initial manifestation of the MID. The patient was of comments and concerns. short stature, had hypoacusis, and had diabetes, which were MIDD, as all mitochondrial disorder (MIDs), is a mito- present long before chorea-ballism occurred. Diabetes must chondrial multiorgan disorder syndrome (MIMODS). have been TI - Maternally inherited diabetes and deafness is a mitochondrial multiorgan disorder syndrome (MIMODS) JF - Acta Diabetologica DO - 10.1007/s00592-017-1029-3 DA - 2017-07-29 UR - https://www.deepdyve.com/lp/springer-journals/maternally-inherited-diabetes-and-deafness-is-a-mitochondrial-XzyVERtkfC SP - 979 EP - 980 VL - 54 IS - 10 DP - DeepDyve ER -