TY - JOUR AU - Wakabayashi, Toshihiko AB - Childs Nerv Syst (2017) 33:1405–1409 DOI 10.1007/s00381-017-3451-9 CASE REPORT Rapid contralateral progression of focal cerebral arteriopathy distinguished from RNF213-related moyamoya disease and fibromuscular dysplasia 1 2 2 3 Yoshio Araki & Yasushi Takagi & Yohei Mineharu & Hatasu Kobayashi & 2 1 Susumu Miyamoto & Toshihiko Wakabayashi Received: 4 March 2017 /Accepted: 2 May 2017 /Published online: 11 May 2017 Springer-Verlag Berlin Heidelberg 2017 . . Abstract Keywords Focal cerebral arteriopathy RNF213 Background Focal cerebral arteriopathy includes unifocal or Moyamoya disease Fibromuscular dysplasia multifocal lesions that are unilateral or bilateral. Large- and/or medium-sized vessels are involved and can be visualized on angiography. Introduction Case report We report a case of cerebral infarction in a 9-year- old Japanese female who presented with a transient ischemic Focal cerebral arteriopathy (FCA) is described as angiographic attack. Steno-occlusion involving the distal part of the internal stenosis that is seen as unilateral or multifocal stenosis of carotid artery, proximal middle cerebral artery, and anterior cere- medium- to large-sized vessels including the terminal portion bral artery was observed. Digital subtraction angiography dem- of the internal carotid artery (ICA), proximal portion of the onstrated a beaded appearance in the cervical portion of the dis- anterior cerebral TI - Rapid contralateral progression of focal cerebral arteriopathy distinguished from RNF213-related moyamoya disease and fibromuscular dysplasia JF - Child's Nervous System DO - 10.1007/s00381-017-3451-9 DA - 2017-05-11 UR - https://www.deepdyve.com/lp/springer-journals/rapid-contralateral-progression-of-focal-cerebral-arteriopathy-Akm2RKJEMB SP - 1405 EP - 1409 VL - 33 IS - 8 DP - DeepDyve ER -