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- Publisher
- American Journal of Neuroradiology
- Copyright
- © 2017 by American Journal of Neuroradiology
- ISSN
- 0195-6108
- eISSN
- 1936-959X
- DOI
- 10.3174/ajnr.A5322
- Publisher site
- See Article on Publisher Site
Abstract
ORIGINAL RESEARCH ADULT BRAIN Basal Ganglia T1 Hyperintensity in Hereditary Hemorrhagic Telangiectasia X A. Parvinian, X V.N. Iyer, X B.S. Pannu, X D.R. Apala, X C.P. Wood, and X W. Brinjikji ABSTRACT BACKGROUND AND PURPOSE: The implications of basal ganglia T1 hyperintensity remain unclear in patients with hereditary hemorrhagic telangiectasia. This study was performed to assess the prevalence of this imaging finding in a large cohort of patients with hereditary hemorrhagic telangiectasia and to identify any association between this phenomenon and other disease manifestations. MATERIALS AND METHODS: In this retrospective study, we identified all patients at our institution diagnosed with definite hereditary hemorrhagic telangiectasia from 2001 to 2017. Patients who did not undergo brain MR imaging were excluded. Patient demographics, laboratory results, and hereditary hemorrhagic telangiectasia disease characteristics were noted. Basal ganglia hyperintensity was evalu- ated both qualitatively and quantitatively relative to the signal intensity in the ipsilateral thalami. Statistical analysis was performed with commercially available software. RESULTS: A total of 312 patients (41% men, 59% women; mean age, 51 18 years) with definite hereditary hemorrhagic telangiectasia were identified. Basal ganglia T1 hyperintensity was present in 23.4% of patients and demonstrated a statistically significant associ- ation with older
Journal
American Journal of Neuroradiology – American Journal of Neuroradiology
Published: Oct 1, 2017