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Simultaneous Medullary Sponge and Adult Polycystic Kidney Disease: The Need for Accurate Diagnosis

Simultaneous Medullary Sponge and Adult Polycystic Kidney Disease: The Need for Accurate Diagnosis Abstract • Two cases of simultaneous medullary sponge and adult polycystic kidney disease developed in siblings. The diagnoses of polycystic kidneys were made by renal ultrasonography and medullary sponge kidney was diagnosed roentgenographically. The family history was markedly positive for "cystic" disease. Medullary sponge kidney might be a precursor of polycystic kidney disease in some instances or, more likely, this represents two separate afflictions occurring in the same individuals. When large medullary sponge kidneys are encountered, the possibility of concomitant polycystic kidney disease should be entertained and investigated with a sonogram. While the prognosis of isolated sponge kidney is excellent, polycystic kidney disease eventually leads to hypertension and renal failure. (Arch Intern Med 1982;142:163-165) References 1. Nemoy NJ, Forsberg L: Polycystic renal disease presenting as medullary sponge kidney. J Urol 1968;100:407-411. 2. Emmett JL, Witten DM: Medullary Sponge Kidney in Clinical Urography , ed 3. Philadelphia, WB Saunders Co, 1971, vol 2, pp 1013-1014. 3. Vespignani L: Sull' associazione delle varie forme della malattia cistica renale. Radiobiol Radiother Fis Med 1951;5:483-498. 4. Hockley BJ, Robinson MF, Tucker WG, et al: Case report: Combined polycystic and medullary sponge renal disease. Australas Radiol 1978;22:315-318.Crossref 5. Cacchi R, Ricci V: Sur une rare maladie que multiples des pyramides rénales le 'rein sponge.' J Urol 1949;55:497-519. 6. Kuiper JJ: Medullary sponge kidney , in Gardner KD Jr (ed): Cystic Diseases of the Kidney . New York, John Wiley & Sons Inc, 1976, pp 151-171. 7. Kissane JM: Adult polycystic disease , in Hamburger J, Crosnier J, Grunfeld JP (eds): Nephrology . New York, John Wiley & Sons Inc, 1979, pp 887-892. 8. Danovitch GM: Polycystic kidney disease , in Gardner KD Jr (ed): Cystic Diseases of the Kidney . New York, John Wiley & Sons Inc, 1976, pp 125-150. 9. Fairley KF, Leighton PW, Kincaid-Smith P: Familial visual defects associated with polycystic kidney and medullary sponge kidney. Br Med J 1963;1:1060-1063.Crossref 10. Vermooten V: Congenital cystic dilatation of the renal collecting tubules: A new disease entity. Yale J Biol Med 1951;23:450-453. 11. Norris RF, Herman L: The pathogenesis of polycystic kidneys: Reconstruction of cystic elements in four cases. J Urol 1961;46:147-174. 12. Hildebrand P: Weiterer beitrag zur pathologischen anatomie der nierengesch wülste: III. Congenitale cystenniere mit sarkombildung. Arch Klin Chir 1894;48:343-371. 13. Kampmeier OF: Hitherto unrecognized mode of origin of congenital renal cysts. Surg Gynecol Obstet 1923;36:208-216. 14. Osathanondh V, Potter EL: Pathogenesis of polycystic kidneys: Type III due to multiple abnormalities of development. Arch Pathol Lab Med 1964;77:485-501. 15. Kuiper JJ: Medullary sponge kidney in three generations. NY State J Med 1971;71:2665-2669. 16. Morris RC, Yamauchi H, Palubinskas AJ, et al: Medullary sponge kidney. Am J Med 1965;38:883-892.Crossref 17. Copping GA: Medullary sponge kidney: Its occurrence in a father and a daughter. Can Med Assoc J 1967;96:608-611. 18. Kliger AS, Schrier RL: Familial disease of the renal medulla: A study of a progeny in a family with medullary cystic disease. Ann Intern Med 1976;95:190-194.Crossref 19. Bennett WB: Kindred coexistence of medullary sponge kidney and medullary cystic disease. Ann Intern Med 1976;85:829.Crossref http://www.deepdyve.com/assets/images/DeepDyve-Logo-lg.png Archives of Internal Medicine American Medical Association

Simultaneous Medullary Sponge and Adult Polycystic Kidney Disease: The Need for Accurate Diagnosis

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References (20)

Publisher
American Medical Association
Copyright
Copyright © 1982 American Medical Association. All Rights Reserved.
ISSN
0003-9926
eISSN
1538-3679
DOI
10.1001/archinte.1982.00340140165030
Publisher site
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Abstract

Abstract • Two cases of simultaneous medullary sponge and adult polycystic kidney disease developed in siblings. The diagnoses of polycystic kidneys were made by renal ultrasonography and medullary sponge kidney was diagnosed roentgenographically. The family history was markedly positive for "cystic" disease. Medullary sponge kidney might be a precursor of polycystic kidney disease in some instances or, more likely, this represents two separate afflictions occurring in the same individuals. When large medullary sponge kidneys are encountered, the possibility of concomitant polycystic kidney disease should be entertained and investigated with a sonogram. While the prognosis of isolated sponge kidney is excellent, polycystic kidney disease eventually leads to hypertension and renal failure. (Arch Intern Med 1982;142:163-165) References 1. Nemoy NJ, Forsberg L: Polycystic renal disease presenting as medullary sponge kidney. J Urol 1968;100:407-411. 2. Emmett JL, Witten DM: Medullary Sponge Kidney in Clinical Urography , ed 3. Philadelphia, WB Saunders Co, 1971, vol 2, pp 1013-1014. 3. Vespignani L: Sull' associazione delle varie forme della malattia cistica renale. Radiobiol Radiother Fis Med 1951;5:483-498. 4. Hockley BJ, Robinson MF, Tucker WG, et al: Case report: Combined polycystic and medullary sponge renal disease. Australas Radiol 1978;22:315-318.Crossref 5. Cacchi R, Ricci V: Sur une rare maladie que multiples des pyramides rénales le 'rein sponge.' J Urol 1949;55:497-519. 6. Kuiper JJ: Medullary sponge kidney , in Gardner KD Jr (ed): Cystic Diseases of the Kidney . New York, John Wiley & Sons Inc, 1976, pp 151-171. 7. Kissane JM: Adult polycystic disease , in Hamburger J, Crosnier J, Grunfeld JP (eds): Nephrology . New York, John Wiley & Sons Inc, 1979, pp 887-892. 8. Danovitch GM: Polycystic kidney disease , in Gardner KD Jr (ed): Cystic Diseases of the Kidney . New York, John Wiley & Sons Inc, 1976, pp 125-150. 9. Fairley KF, Leighton PW, Kincaid-Smith P: Familial visual defects associated with polycystic kidney and medullary sponge kidney. Br Med J 1963;1:1060-1063.Crossref 10. Vermooten V: Congenital cystic dilatation of the renal collecting tubules: A new disease entity. Yale J Biol Med 1951;23:450-453. 11. Norris RF, Herman L: The pathogenesis of polycystic kidneys: Reconstruction of cystic elements in four cases. J Urol 1961;46:147-174. 12. Hildebrand P: Weiterer beitrag zur pathologischen anatomie der nierengesch wülste: III. Congenitale cystenniere mit sarkombildung. Arch Klin Chir 1894;48:343-371. 13. Kampmeier OF: Hitherto unrecognized mode of origin of congenital renal cysts. Surg Gynecol Obstet 1923;36:208-216. 14. Osathanondh V, Potter EL: Pathogenesis of polycystic kidneys: Type III due to multiple abnormalities of development. Arch Pathol Lab Med 1964;77:485-501. 15. Kuiper JJ: Medullary sponge kidney in three generations. NY State J Med 1971;71:2665-2669. 16. Morris RC, Yamauchi H, Palubinskas AJ, et al: Medullary sponge kidney. Am J Med 1965;38:883-892.Crossref 17. Copping GA: Medullary sponge kidney: Its occurrence in a father and a daughter. Can Med Assoc J 1967;96:608-611. 18. Kliger AS, Schrier RL: Familial disease of the renal medulla: A study of a progeny in a family with medullary cystic disease. Ann Intern Med 1976;95:190-194.Crossref 19. Bennett WB: Kindred coexistence of medullary sponge kidney and medullary cystic disease. Ann Intern Med 1976;85:829.Crossref

Journal

Archives of Internal Medicine – American Medical Association

Published: Jan 1, 1982

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