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PECULIAR DEFORMITY OF HANDS OCCURRING IN EPIDERMOLYSIS BULLOSA

PECULIAR DEFORMITY OF HANDS OCCURRING IN EPIDERMOLYSIS BULLOSA Abstract THE DISEASE known as epidermolysis bullosa was first described by Tilbury Fox in 1879.1 Since then many case reports have been published, and, although the disease is rare, individual cases are not now worthy of reporting unless they present some unusual feature. Efforts of classification into congenital types and acquired types, hereditary or nonhereditary, have been repeatedly made. Tulipan2 divided the chief types into three groups: simplex, dystrophica (dominant) and dystrophica (recessive), according to the clinical features. Becker and Obermayer3 recognized only two forms: epidermolysis bullosa simplex and epidermolysis bullosa dystrophica. Most recorded cases have presented the following common features: The condition appears at birth, or shortly afterward, and bullae appear in response to slight trauma and most frequently on the parts most exposed to trauma—the extremities, especially near joints. We herein report a rare case showing a peculiar deformity of the hands resulting from References 1. Fox, T.: Congenital Ulceration of Skin (Two Cases) with Pemphigus Eruption and Arrest of Development Generally , Lancet 1:766, 1879.Crossref 2. Tulipan, L.: Epidermolysis Bullosa Dystrophica (Recessive Type): Report of Case , Arch. Dermat. & Syph. 37:22 ( (Jan.) ) 1938. 3. Becker, W. S., and Obermayer, M. E.: Modern Dermatology and Syphilology , ed. 2, Philadelphia, J. B. Lippincott Company, 1947, p. 73. 4. Guy, W. H.: Epidermolysis Bullosa , Arch. Dermat. & Syph. 15:30 ( (Jan.) ) 1927. 5. Calhoun, T. S., and Brown, W. P.: Epidermolysis Bullosa , Arch. Dermat. & Syph. 11:185 ( (Feb.) ) 1925. 6. Touraine, A., and Dereu, C.: Congenital Bullous Epidermolysis (Dystrophic type) , Bull. Soc. franç. de dermat. et syph. 47:41 ( (Feb.) ) 1940. 7. Tobias, N.: Lesions of the Mucus Membranes in Epidermolysis Bullosa , Arch. Dermat. & Syph. 18:224 ( (Aug.) ) 1928. 8. Smith, S. F.: Epidermolysis Bullosa Non-Hereditaria, Non-Congenita , Urol. & Cutan. Rev. 31:243 ( (April) ) 1927. 9. Turner, W. J., and Obermayer, M. E.: Studies on Porphyria: II. A Case of Porphyria Accompanied with Epidermolysis Bullosa, Hypertrichosis and Melanosis , Arch. Dermat. & Syph. 37:549 ( (April) ) 1938. 10. Zeligman, I., and Baum, M.: Porphyric Bullous Dermatitis , Arch. Dermat. & Syph. 58:4 ( (Oct.) ) 1948. 11. Cannon, B. A.; Sanders, M., and Rankin, J. L.: Epidermolysis Bullosa: A Clinical and Bacteriologic Study; Report of Four Cases , Arch. Dermat. & Syph. 42:884 ( (Nov.) ) 1940. 12. Waddill, G. M., Jr.: Epidermolysis Bullosa Hereditaria , J. Pediat. 16:500 ( (April) ) 1940. http://www.deepdyve.com/assets/images/DeepDyve-Logo-lg.png Archives of Dermatology and Syphilology American Medical Association

PECULIAR DEFORMITY OF HANDS OCCURRING IN EPIDERMOLYSIS BULLOSA

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References (15)

Publisher
American Medical Association
Copyright
Copyright © 1950 American Medical Association. All Rights Reserved.
ISSN
0096-6029
DOI
10.1001/archderm.1950.01530150102012
Publisher site
See Article on Publisher Site

Abstract

Abstract THE DISEASE known as epidermolysis bullosa was first described by Tilbury Fox in 1879.1 Since then many case reports have been published, and, although the disease is rare, individual cases are not now worthy of reporting unless they present some unusual feature. Efforts of classification into congenital types and acquired types, hereditary or nonhereditary, have been repeatedly made. Tulipan2 divided the chief types into three groups: simplex, dystrophica (dominant) and dystrophica (recessive), according to the clinical features. Becker and Obermayer3 recognized only two forms: epidermolysis bullosa simplex and epidermolysis bullosa dystrophica. Most recorded cases have presented the following common features: The condition appears at birth, or shortly afterward, and bullae appear in response to slight trauma and most frequently on the parts most exposed to trauma—the extremities, especially near joints. We herein report a rare case showing a peculiar deformity of the hands resulting from References 1. Fox, T.: Congenital Ulceration of Skin (Two Cases) with Pemphigus Eruption and Arrest of Development Generally , Lancet 1:766, 1879.Crossref 2. Tulipan, L.: Epidermolysis Bullosa Dystrophica (Recessive Type): Report of Case , Arch. Dermat. & Syph. 37:22 ( (Jan.) ) 1938. 3. Becker, W. S., and Obermayer, M. E.: Modern Dermatology and Syphilology , ed. 2, Philadelphia, J. B. Lippincott Company, 1947, p. 73. 4. Guy, W. H.: Epidermolysis Bullosa , Arch. Dermat. & Syph. 15:30 ( (Jan.) ) 1927. 5. Calhoun, T. S., and Brown, W. P.: Epidermolysis Bullosa , Arch. Dermat. & Syph. 11:185 ( (Feb.) ) 1925. 6. Touraine, A., and Dereu, C.: Congenital Bullous Epidermolysis (Dystrophic type) , Bull. Soc. franç. de dermat. et syph. 47:41 ( (Feb.) ) 1940. 7. Tobias, N.: Lesions of the Mucus Membranes in Epidermolysis Bullosa , Arch. Dermat. & Syph. 18:224 ( (Aug.) ) 1928. 8. Smith, S. F.: Epidermolysis Bullosa Non-Hereditaria, Non-Congenita , Urol. & Cutan. Rev. 31:243 ( (April) ) 1927. 9. Turner, W. J., and Obermayer, M. E.: Studies on Porphyria: II. A Case of Porphyria Accompanied with Epidermolysis Bullosa, Hypertrichosis and Melanosis , Arch. Dermat. & Syph. 37:549 ( (April) ) 1938. 10. Zeligman, I., and Baum, M.: Porphyric Bullous Dermatitis , Arch. Dermat. & Syph. 58:4 ( (Oct.) ) 1948. 11. Cannon, B. A.; Sanders, M., and Rankin, J. L.: Epidermolysis Bullosa: A Clinical and Bacteriologic Study; Report of Four Cases , Arch. Dermat. & Syph. 42:884 ( (Nov.) ) 1940. 12. Waddill, G. M., Jr.: Epidermolysis Bullosa Hereditaria , J. Pediat. 16:500 ( (April) ) 1940.

Journal

Archives of Dermatology and SyphilologyAmerican Medical Association

Published: Aug 1, 1950

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